“They don’t understand the urgency,” Donavon Decker said about the need to find treatments for the rare disease limb-girdle muscular dystrophy.Courtesy Muscular Dystrophy Association

Jason Mast is a general assignment reporter at STAT focused on the science behind new medicines and the systems and people that decide whether that science ever reaches patients. You can reach Jason on Signal at JasonMast.05.

On Thanksgiving Day 1998, a geneticist called Donavon Decker and told him the lab had identified the gene that was causing his and his sisters’ muscles to slowly deteriorate. By the way, the geneticist added, this might be a good candidate for gene therapy.

Decker called back every month until April, when the researcher finally put him in touch with neurologist Jerry Mendell. Mendell said Decker could be of service — but that he couldn’t help Decker. 

Advertisement

Gene therapy was still new and risky. No muscular dystrophy patient had ever received one. To assure safety, Mendell would only inject a tiny foot muscle. Decker wouldn’t benefit. He could be harmed and might be rendered ineligible for future gene therapies. But if it worked, it could advance the field, including for his four sisters with the disease.

STAT+ Exclusive Story

STAT+

This article is exclusive to STAT+ subscribers

Unlock this article — plus daily coverage and analysis of the biotech sector — by subscribing to STAT+.

Already have an account? Log in

Monthly

$39

Totals $468 per year

$39/month Get Started

Totals $468 per year

Starter

$30

for 3 months, then $399/year

$30 for 3 months Get Started

Then $399/year

Annual

$399

Save 15%

$399/year Get Started

Save 15%

11+ Users

Custom

Savings start at 25%!

Request A Quote Request A Quote

Savings start at 25%!

2-10 Users

$300

Annually per user

$300/year Get Started

$300 Annually per user

View All Plans

To read the rest of this story subscribe to STAT+.

Subscribe